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CC BY 4.0 · European J Pediatr Surg Rep. 2021; 09(01): e51-e55
DOI: 10.1055/s-0041-1728725
Case Report

Anorectal Malformation with Rectovestibular Fistula and Vaginal Agenesis: Usage of Rectovestibular Fistula as a Neovagina Followed by PSARP with Preservation of the Anal Sphincter

Antonio Dessanti
1   AOU University Hospital, University of Sassari, Sassari, Italy
,
Osnel Louisma
2   Department of Pediatric Surgery, Saint Damien Children Hospital, Port Au Prince, Haiti
,
Gabriel Steve Pierre
2   Department of Pediatric Surgery, Saint Damien Children Hospital, Port Au Prince, Haiti
,
Nguhien Thanh Liem
3   Department of Pediatric Surgery, National Children Hospital and Vinmec International Hospital, Hanoi, Vietnam
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Abstract

Anorectal malformation with rectovestibular fistula associated with vaginal agenesis is rare. We report on a child in whom this combination was diagnosed at the age of 1 year. After creation of a divided descending colostomy, we chose to leave the rectum-rectovestibular fistula to function as a neovagina, while the sigmoid colon was relocated via modified posterior sagittal anorectoplasty. The colostomy was closed 6 months after the main surgery. After a follow-up of 3 years, the patient is continent for stool and urine. The introitus of the neovagina appears wide and easy to explore. We conclude that our surgical approach may be a good option for these children.

Keywords

anorectal malformation - vaginal agenesis - posterior sagittal anorectoplasty - vaginoplasty


Publication History

Received: 18 June 2020

Accepted: 06 March 2021

Article published online:
12 July 2021

© 2021. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. (https://creativecommons.org/licenses/by/4.0/)

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