CC BY 4.0 · European J Pediatr Surg Rep. 2021; 09(01): e9-e12
DOI: 10.1055/s-0040-1721469
Case Report

Congenital Anterior Urethrocutaneous Fistula with a Persistent Urethral Groove

1  Department of Paediatric Urology, Evelina London Children's Hospital, London, United Kingdom
,
Massimo Garriboli
1  Department of Paediatric Urology, Evelina London Children's Hospital, London, United Kingdom
› Author Affiliations

Abstract

Congenital anterior urethrocutaneous fistula (CAUF) is a rare penile anomaly with only 63 cases reported in the literature. The anomaly can present in isolation or in association with chordee or hypospadias. We report the case of an 8-month-old boy with CAUF that resembles the embryological urethral groove. On examination, a wide urethral groove was noted to cover the midshaft of the penis with a well formed urethra extending proximally and distally and with a normal glandular anatomy, a wide glandular meatus, and a complete foreskin. The urethral groove was tubularized and covered in layers. Surgery was complicated with early superficial skin dehiscence not affecting the urethral repair.

Refashioning of the skin was then performed. A satisfactory aesthetic and functional outcome was observed at 7 years' follow-up. Defining the anatomy of CAUF and distal urethra is key in management of these children.



Publication History

Received: 15 May 2020

Accepted: 09 October 2020

Publication Date:
29 January 2021 (online)

© 2021. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution License, permitting unrestricted use, distribution, and reproduction so long as the original work is properly cited. (https://creativecommons.org/licenses/by/4.0/)

Georg Thieme Verlag KG
Rüdigerstraße 14, 70469 Stuttgart, Germany