Journal of Pediatric Neurology 2021; 19(05): 343-347
DOI: 10.1055/s-0040-1718777
Case Report

Retrocerebellar Ependymal Cyst Presenting with Obstructive Hydrocephalus in an Infant

1   Department of Neurosurgery, 12 de Octubre University Hospital, Madrid, Spain
,
Pablo Martin Munarriz
1   Department of Neurosurgery, 12 de Octubre University Hospital, Madrid, Spain
,
Aurelio Hernandez Lain
2   Department of Pathological Anatomy, 12 de Octubre University Hospital, Madrid, Spain
,
Carla Eiriz Fernández
1   Department of Neurosurgery, 12 de Octubre University Hospital, Madrid, Spain
,
Daniel Garcia Pérez
1   Department of Neurosurgery, 12 de Octubre University Hospital, Madrid, Spain
,
Luis Miguel Moreno Gómez
1   Department of Neurosurgery, 12 de Octubre University Hospital, Madrid, Spain
,
Olga Estaban Sinovas
1   Department of Neurosurgery, 12 de Octubre University Hospital, Madrid, Spain
,
Beatriz Pascual
1   Department of Neurosurgery, 12 de Octubre University Hospital, Madrid, Spain
,
Alfonso Lagares Abascal
1   Department of Neurosurgery, 12 de Octubre University Hospital, Madrid, Spain
› Institutsangaben

Abstract

Intracranial ependymal cysts (ECs) are rare benign lesions. They are frequently asymptomatic and arise in the supratentorial regions. Retrocerebellar ECs is a rare location. We present a case of 3-months-old infant who developed obstructive hydrocephalus, bulging fontanel, and macrocephaly secondary to a retrocerebellar EC. Magnetic resonance imaging (MRI) showed a large retrocerebellar cyst that compressed the cerebellum and the brainstem, producing fourth ventricle outlet obstruction and supratentorial hydrocephalus. Microsurgical fenestration of the cyst to the obex of the fourth ventricle and a cystic wall biopsy were performed. The procedure improved supratentorial hydrocephalus, as well as the patient's clinical condition. A histopathological study confirmed the diagnosis of an EC.

As far as we know, after a thorough review of the literature, this is the first reported case of retrocerebellar EC. It is a rare cause of hydrocephalus due to outlet obstruction of the fourth ventricle. Treatment of the cause itself was shown to be effective.



Publikationsverlauf

Eingereicht: 21. Juli 2020

Angenommen: 11. September 2020

Artikel online veröffentlicht:
26. Oktober 2020

© 2020. Thieme. All rights reserved.

Georg Thieme Verlag KG
Rüdigerstraße 14, 70469 Stuttgart, Germany

 
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