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CC BY-NC-ND 4.0 · Indian Journal of Neurotrauma 2021; 18(01): 69-71
DOI: 10.1055/s-0040-1718245
Case Report

Klippel–Feil Syndrome with Multiple Cervical Anomalies Discovered Following Trauma

Fernando Celi
1   Department of Neurosurgery, Hospital de Emergencias José Casimiro Ulloa, Miraflores, Lima, Perú
,
Giancarlo Saal-Zapata
2   Department of Neurosurgery, Hospital Nacional Guillermo Almenara Irigoyen, La Victoria, Lima, Perú
3   Clínica Angloamericana, San Isidro, Lima, Perú
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Abstract

The approach to the upper cervical spine is a challenge for surgeons, not only for its complex anatomy but also for the great variety of pathologies. Klippel–Feil syndrome (KFS) is a congenital disease characterized by the fusion of two or more cervical segments and is associated with various musculoskeletal and vascular malformations. However, there is no consensus on the type of surgery, approach, level of fixation or fusion. We report the case of a KFS, associated with multiple anatomical variants, who suffered a traumatic cervical injury and underwent surgical treatment.

Keywords

Klippel–Feil syndrome - atlas - vertebral artery - cervical fracture - anterior cervical corpectomy and fusion


Publication History

Article published online:
09 October 2020

© 2020. Neurotrauma Society of India. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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