CC BY-NC-ND 4.0 · Journal of Health and Allied Sciences NU 2021; 11(01): 40-43
DOI: 10.1055/s-0040-1718237
Case Report

An Interesting Case of Bilateral Upper Limb Wasting: Hirayama Disease

Priscilla Rubavathy Eugin
1  Department of General Medicine, Sri Manakula Vinayagar Medical College and Hospital, Pondicherry, India
,
Manokaran Chinnusamy
1  Department of General Medicine, Sri Manakula Vinayagar Medical College and Hospital, Pondicherry, India
,
Sathiyanarayanan Janakiraman
1  Department of General Medicine, Sri Manakula Vinayagar Medical College and Hospital, Pondicherry, India
› Author Affiliations

Abstract

Hirayama disease is a rare neurologic disease and is characterized by insidious unilateral or bilateral muscular atrophy and weakness of the forearms and hands without sensory or pyramidal signs. Our patient presented with bilateral upper limb wasting, which is a rarer variant of motor neuron disease. The diagnosis of Hirayama disease is based on dynamic magnetic resonance imaging (MRI). This case displays how dynamic cervical spine MRI can pick up dynamic cord compression and contributes to zero in the diagnosis of Hirayama disease.



Publication History

Publication Date:
16 October 2020 (online)

© 2020. Nitte University (Deemed to be University). This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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