An Interesting Case of Bilateral Upper Limb Wasting: Hirayama Disease
Hirayama disease is a rare neurologic disease and is characterized by insidious unilateral or bilateral muscular atrophy and weakness of the forearms and hands without sensory or pyramidal signs. Our patient presented with bilateral upper limb wasting, which is a rarer variant of motor neuron disease. The diagnosis of Hirayama disease is based on dynamic magnetic resonance imaging (MRI). This case displays how dynamic cervical spine MRI can pick up dynamic cord compression and contributes to zero in the diagnosis of Hirayama disease.
16 October 2020 (online)
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