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CC BY-NC-ND 4.0 · Annals of Otology and Neurotology 2020; 3(01): 38-41
DOI: 10.1055/s-0040-1715292
Case Report

Goldenhar Syndrome Presenting As Squamosal Chronic Otitis Media

Ravi Ambewadi
1   Department of Otolaryngology, Head and Neck Surgery, Karnataka Institute of Medical Sciences, Hubli, Karnataka, India
,
Vikram Kemmannu Bhat
1   Department of Otolaryngology, Head and Neck Surgery, Karnataka Institute of Medical Sciences, Hubli, Karnataka, India
,
Prajna Laxman Salian
1   Department of Otolaryngology, Head and Neck Surgery, Karnataka Institute of Medical Sciences, Hubli, Karnataka, India
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Abstract

Goldenhar syndrome is a rare congenital anomaly involving the eye, ear, vertebra, and the mandible. This anomaly presenting primarily to the ENT outpatient clinic with ear discharge and cholesteatoma is still rarer. Here we describe one such rare case that was a challenge to diagnose as well as manage. We also discuss the various problems in the management and highlight the need for a multispecialty approach to tackling the various pathologies in such a case.

Keywords

hearing loss - otitis media - Goldenhar syndrome


Publication History

Article published online:
29 July 2020

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