Abstract
Preiser disease is a rare condition of avascular necrosis of the scaphoid occurring
in the absence scaphoid fracture or trauma. While the etiology of Preiser disease
remains unknown, it has been associated with steroid use, chemotherapy, and infrequently
with systemic diseases. No reports have associated Preiser disease with hemoglobinopathy.
Due to the rarity of Preiser disease, management remains controversial and evidence
is limited. Here, we describe the case of a 32-year-old right-hand dominant male with
sickle cell anemia and a 4-year history of bilateral wrist pain. Radiographs and gadolinium-enhanced
magnetic resonance imaging revealed bilateral Preiser disease. He was successfully
managed with a 1,2 intercompartmental supraretinicaular artery vascularized bone graft
to the right scaphoid.
Keywords
Preiser disease - hemoglobinopathy - sickle cell disease - vascularized bone grafts
