CC BY-NC-ND 4.0 · Arquivos Brasileiros de Neurocirurgia: Brazilian Neurosurgery 2020; 39(03): 239-242
DOI: 10.1055/s-0040-1713919
Case Report | Relato de Caso

Adult Nasoethmoidal Encephalocele Corrected by Supraorbitary Approach: Case Report and Review

Encefalocele nasoetmoidal de adulto corrigida por acesso supraorbitário: Relato de caso e revisão de literatura
Francisco Fernando Dacier Teixeira
1   Departament of Neurosurgery of the Faculdade de Medicina de São José do Rio Preto, São José do Rio Preto, SP, Brazil
,
Raysa Moreira Aprígio
1   Departament of Neurosurgery of the Faculdade de Medicina de São José do Rio Preto, São José do Rio Preto, SP, Brazil
,
Dionei Freitas de Moraes
1   Departament of Neurosurgery of the Faculdade de Medicina de São José do Rio Preto, São José do Rio Preto, SP, Brazil
,
Mário José Góes
1   Departament of Neurosurgery of the Faculdade de Medicina de São José do Rio Preto, São José do Rio Preto, SP, Brazil
,
Feres Chaddad-Neto
2   Departament of Neurosurgery, Universidade Federal de São Paulo, São Paulo, SP, Brazil
,
Ricardo Lourenço Caramanti
1   Departament of Neurosurgery of the Faculdade de Medicina de São José do Rio Preto, São José do Rio Preto, SP, Brazil
› Author Affiliations

Abstract

Encephalocele is a protrusion of the central nervous system elements through a defect in the dura mater and in the cranium. The prevalence of encephalocele ranges from 0.08 to 0.5 per 1,000 births. The posterior encephaloceles are more common in North America and Europe, while frontal defect is frequently found in Asia. The present paper describes a 26-year-old male patient presenting with cerebrospinal fluid leak and meningitis symptoms. He was diagnosed with congenital nasoethmoidal encephalocele and treated surgically using a supraorbital approach without complications.

Resumo

Encefalocele é definida como uma protrusão dos elementos do sistema nervoso central por um defeito localizado na dura máter no crânio. Sua prevalência apresenta-se entre 0.08 e 0.5 casos a cada 1.000 nascimentos. As encefaloceles posteriores são mais comuns na América do Norte e na Europa, já os defeitos frontais são frequentemente encontrados na Ásia. O presente artigo descreve o caso de um paciente do sexo masculino de 26 anos de idade com quadro de fístula liquórica nasal associada a meningite de repetição. Ele foi diagnosticado com encefalocele nasoetmoidal congênita, e tratado de forma cirúrgica com um acesso via supraorbital, sendo realizada a correção completa da falha sem intercorrências.



Publication History

Received: 31 March 2020

Accepted: 12 May 2020

Article published online:
31 July 2020

© 2020. The Author(s). This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

Thieme Revinter Publicações Ltda
Rio de Janeiro, Brazil

 
  • References

  • 1 Mahajan C, Rath GP, Bithal PK, Mahapatra AK. Perioperative Management of Children With Giant Encephalocele: A Clinical Report of 29 Cases. J Neurosurg Anesthesiol 2017; 29 (03) 322-329
  • 2 Gandhoke GS, Goldschmidt E, Kellogg R, Greene S. Encephalocele development from a congenital meningocele: case report. J Neurosurg Pediatr 2017; 20 (05) 419-422
  • 3 Suwanwela C, Suwanwela N. A morphological classification of sincipital encephalomeningoceles. J Neurosurg 1972; 36 (02) 201-211
  • 4 Suwanwela C, Hongsaprabhas C. Fronto-ethmoidal encephalomeningocele. J Neurosurg 1966; 25 (02) 172-182
  • 5 Santos-Franco JA, Dávila-Romero J, Rangel-Morales C, Sandoval-Balanzario M, Lee A. Obstrucción nasal crónica: encefalocele nasoetmoidal em paciente adulto. Gac Med Mex 2010; 146 (04) 291-293
  • 6 Arifin M, Suryaningtyas W, Bajamal AH. Frontoethmoidal encephalocele: clinical presentation, diagnosis, treatment, and complications in 400 cases. Childs Nerv Syst 2018; 34 (06) 1161-1168
  • 7 Mahatumarat C, Rojvachiranonda N, Taecholarn C. Frontoethmoidal encephalomeningocele: surgical correction by the Chula technique. Plast Reconstr Surg 2003; 111 (02) 556-565 , discussion 566–567
  • 8 Rojvachiranonda N, David DJ, Moore MH, Cole J. Frontoethmoidal encephalomeningocele: new morphological findings and a new classification. J Craniofac Surg 2003; 14 (06) 847-858
  • 9 Zoghlami A, Bon Mardion N, Callonnec F, Dehesdin D, Proust F, Marie JP. Transalar transsphenoidal meningoencephalocele presenting in the form of recurrent meningitis: Report of two cases and discussion of the diagnosis and treatment. Eur Ann Otorhinolaryngol Head Neck Dis 2016; 133 (06) 423-427
  • 10 Hassanein AG, Fadle KN. Single-stage combined craniofacial repair for frontoethmoidal meningoencephalocele. J Craniofac Surg 2017; 28 (01) e9-e12
  • 11 Smith DE, Murphy MJ, Hitchon PW, Babin RW, Abu-Yousef MM. Transsphenoidal encephaloceles. Surg Neurol 1983; 20 (06) 471-480
  • 12 Donnenfeld AE, Hughes H, Weiner S. Prenatal diagnosis and perinatal management of frontoethmoidal meningoencephalocele. Am J Perinatol 1988; 5 (01) 51-53
  • 13 Boonvisut S, Ladpli S, Sujatanond M. , et al. Morphologic study of 120 skull base defects in frontoethmoidal encephalomeningoceles. Plast Reconstr Surg 1998; 101 (07) 1784-1795
  • 14 Leelanukrom R, Wacharasint P, Kaewanuchit A. Perioperative management for surgical correction of frontoethmoidal encephalomeningocele in children: a review of 102 cases. Paediatr Anaesth 2007; 17 (09) 856-862
  • 15 Warf BC, Stagno V, Mugamba J. Encephalocele in Uganda: ethnic distinctions in lesion location, endoscopic management of hydrocephalus, and survival in 110 consecutive children. J Neurosurg Pediatr 2011; 7 (01) 88-93
  • 16 Mahapatra AK, Suri A. Anterior encephaloceles: a study of 92 cases. Pediatr Neurosurg 2002; 36 (03) 113-118
  • 17 Gumussoy M, Ugur O, Cukurova I, Uluyol S. Recurrent meningitis and frontal encephalocele as delayed complications of craniofacial trauma. J Craniofac Surg 2014; 25 (02) 529-530
  • 18 Dodge Jr HW, Love JG, Kernohan JW. Intranasal encephalomeningoceles associated with cranium bifidum. AMA Arch Surg 1959; 79 (01) 75-84
  • 19 Gun R, Tosun F, Durmaz A. , et al. Predictors of surgical approaches for the repair of anterior cranial base encephaloceles. Eur Arch Otorhinolaryngol 2013; 270 (04) 1299-1305