CC BY-NC-ND 4.0 · Journal of Health and Allied Sciences NU 2016; 06(04): 95-98
DOI: 10.1055/s-0040-1708685
Case Report

Steroid Cell Tumour - A Rare Cause of Hirsuitism in a Female

Sruthi M. Kumar
1   Post Graduate, Department of Obstetrics and Gynaecology, K.S. Hegde Hospital, Mangalore
,
Aparna Rajesh
2   Associate Professor, Department of Obstetrics and Gynaecology, K.S. Hegde Hospital, Mangalore
,
Harish Shetty
3   HOD and Professor, Department of Obstetrics and Gynaecology, K.S. Hegde Hospital, Mangalore
› Author Affiliations

Abstract

Steroid cell tumours of the ovary account for < 0.1 % of all the ovarian tumours. It is a functioning sex cord stromal tumour. Previously designated as lipoid cell tumours, one-third of these tumours are considered malignant with the mean age of presentation at around 40 years. We present a case of 20 year old unmarried girl with regular cycles who came with sudden onset amenorrhea, hirsuitism, abdominal distension and signs of virilizationof 5 month duration and recent onset of dyspnea to Obstetrics and Gynaecology outpatient department. Moderate ascites was present. Clinical and radiological evaluation revealed a right adnexal mass with elevated serum testosterone. She was diagnosed with right ovarian benign functioning tumour and underwent right sapling oophorectomy. Histopathology confirmed the diagnosis. 2 weeks post operatively her testosterone levels decreased. Surgery is the treatment of steroid cell tumours although medical therapy using Gonadotrophin Releasing Hormone [GnRH] analogues has been tried recently in recurrent or inoperable cases.



Publication History

Received: 11 April 2016

Accepted: 04 November 2016

Article published online:
22 April 2020

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