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CC BY-NC-ND 4.0 · Journal of Health and Allied Sciences NU 2016; 06(03): 45-47
DOI: 10.1055/s-0040-1708662
Case Report

Anaesthesia management in a child with Apert syndrome with craniosynostosis

Leena Harshad Parate
1   Assistant professor, Department of Anaesthesia, M.S. Ramaiah Medical Collage, Banagalore
,
M.C. Nagaraj
2   Professor, Department of Anaesthesia, M.S. Ramaiah Medical Collage, Banagalore
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Abstract

Apert syndrome is a rare congenial anomaly with multisystem involvement. It is characterized by craniosynostosis, midfacial hypoplasia and global syndactyly. Altered upper and lower airway anatomy, multiple visceral anomalies and multiple repeat surgeries are main anaesthetic challenges. Here we report a case of seven month old child with Apert syndrome who was posted for posterior sagittal anorectoplasty.

Keywords

Apert syndrome - craniosynostosis - anaesthesia


Publication History

Received: 18 August 2016

Accepted: 17 August 2016

Article published online:
27 June 2020

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