CC BY-NC-ND 4.0 · Journal of Health and Allied Sciences NU 2014; 04(02): 149-151
DOI: 10.1055/s-0040-1703788
Case Report

A RARE CASE OF CYANOSIS AND CLUBBING –LIVER INDUCED VASCULAR DISORDER OF LUNG

Pothukuchi Venkata Krishna
1  Professor, Department of General Medicine Guntur Medical College, Government General Hospital, Guntur, Andhra Pradesh, India
,
Manasa Manne
2  P. G. Students, Department of General Medicine Guntur Medical College, Government General Hospital, Guntur, Andhra Pradesh, India
,
Venkata Ravikumar Chepuri
2  P. G. Students, Department of General Medicine Guntur Medical College, Government General Hospital, Guntur, Andhra Pradesh, India
› Author Affiliations

Abstract:

The hepatopulmonary syndrome (HPS) is under recognized complication of chronic liver disease. Hepatopulmonary syndrome has three components: liver disease, pulmonary vascular dilatation, and a defect in oxygenation. If hypoxemia and dyspnea develop in these patients in the absence of known intrinsic cardiopulmonary disorder, the hepatopulmonary syndrome must be considered. Clinical features include digital clubbing, cyanosis, spider neavi. It is a rare complication of liver disease of varied etiology and indicates a poor prognosis. We are reporting a case of severe clubbing of fingers associated with severe cyanosis and chronic liver disorder in a very young girl to highlight that other causes also should be thought of in addition to cyanotic congenital heart disease in such a young age.



Publication History

Publication Date:
24 April 2020 (online)

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