J Neurol Surg A Cent Eur Neurosurg 2020; 81(04): 372-376
DOI: 10.1055/s-0040-1701622
Case Report
Georg Thieme Verlag KG Stuttgart · New York

Case Report of Cerebellar Endometriosis

Michael Meggyesy
1   Department of Neurosurgery, Asklepios Klinik Altona, Hamburg, Germany
,
Michael Friese
2   Department of Neuropathology, Asklepios Kliniken Hamburg GmbH Asklepios Klinik Nord Standort Heidberg, Hamburg, Hamburg, Germany
,
Joachim Gottschalk
2   Department of Neuropathology, Asklepios Kliniken Hamburg GmbH Asklepios Klinik Nord Standort Heidberg, Hamburg, Hamburg, Germany
,
Uwe Kehler
1   Department of Neurosurgery, Asklepios Klinik Altona, Hamburg, Germany
› Author Affiliations
Further Information

Publication History

23 April 2019

03 July 2019

Publication Date:
28 March 2020 (online)

Abstract

Endometriosis is a disorder in women which is characterized by extrauterine manifestations. We describe a case of cerebellar endometriosis in a 39-year-old woman who underwent posterior fossa decompression multiple times without establishing a correct diagnosis. Her neurologic status progressively worsened due to chronic hydrocephalus and brainstem compression by cysts. Late in the clinical course, histology from the cyst wall was taken that revealed endometriosis with clear cells and positive immunohistology for progesterone and estrogen receptors. Treatment with gestagens was started but did not improve the patient's status. In patients with chronic recurring intracranial cysts and hydrocephalus, cerebral endometriosis should be considered.