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CC BY-NC-ND 4.0 · Ann Natl Acad Med Sci 2019; 55(04): 213-218
DOI: 10.1055/s-0039-3402665
Case Report

Gorlin–Goltz Syndrome with Multidisciplinary Approach of Treatment

Jayachandran Sadaksharam
1   Department of Oral Medicine and Radiology, Tamil Nadu Government Dental College and Hospital, Chennai, Tamil Nadu, India
,
Amutha Velappan Annapoorni
1   Department of Oral Medicine and Radiology, Tamil Nadu Government Dental College and Hospital, Chennai, Tamil Nadu, India
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Abstract

Gorlin–Goltz syndrome, is an uncommon genetic condition characterized by the presence of multiple odontogenic keratocysts of jaws along with several other abnormal, cutaneous, ophthalmic, and osseous displays. This syndrome is also acknowledged by various names, such as nevoid basal cell carcinoma syndrome, jaw cyst, and bifid rib syndrome. This article illustrates about the clinical, radiological, and histological diagnostic findings and the multidisciplinary approach of treatment given to one such rare case of Gorlin–Goltz syndrome.

Keywords

Gorlin–Goltz syndrome - multiple odontogenic keratocyst syndrome - nevoid basal cell carcinoma syndrome - Gorlin’s syndrome


Publication History

Article published online:
27 January 2020

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