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CC BY-NC-ND 4.0 · Journal of Gastrointestinal and Abdominal Radiology 2020; 3(S 01): S49-S53
DOI: 10.1055/s-0039-3402611
Case Report

Venous Tumor Thrombosis and Pulmonary Metastases in a Case of Adrenal Neuroblastoma—Occurrence of Two Rare Manifestations in a Single Patient: Case Report and Review of Literature

Somesh Singh
1   Department of Radiodiagnosis, Tata Memorial Centre, Mumbai, India
,
Seema Kembhavi
1   Department of Radiodiagnosis, Tata Memorial Centre, Mumbai, India
,
Sneha Shah
2   Department of Nuclear Medicine, Tata Memorial Centre, Mumbai, India
,
Tushar Vora
3   Department of Paediatric Oncology, Tata Memorial Centre, Mumbai, India
,
Girish Chinnaswamy
3   Department of Paediatric Oncology, Tata Memorial Centre, Mumbai, India
,
Sajid Qureshi
4   Department of Paediatric Surgical Oncology, Tata Memorial Centre, Mumbai, India
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Abstract

Unlike other pediatric extra cranial solid neoplasms, neuroblastomas have very low incidence of pulmonary metastases. Neuroblastomas also tend to encase rather than infiltrate the major vessels with very low incidence of tumor thrombus. Even in cases with inferior vena cava tumor thrombosis, pulmonary metastases are a rare occurrence. These patients usually show widespread disseminated disease at presentation. We present a rare case of adrenal neuroblastoma with tumor thrombus and bilateral pulmonary metastases at presentation. This presentation can be confused with adrenocortical carcinoma and differentiating between the two is essential for further management.

Keywords

neuroblastoma - pulmonary metastases - tumor thrombosis


Publication History

Article published online:
11 May 2020

© 2020. Indian Society of Gastrointestinal and Abdominal Radiology. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/).

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