Segmental Arterial Mediolysis with Supra-Aortic Vascular Involvement: Report of Two Cases

Abstract

Segmental arterial mediolysis (SAM) is a rare noninflammatory vasculopathy predominantly involving the visceral arteries of the abdomen. The most common presentation described is massive intra-abdominal hemorrhage secondary to aneurysm rupture. In this report, we describe two cases with characteristic findings of aneurysm, dissection, and beading involving the visceral arteries and the supra-aortic vessels. SAM involving the supra-aortic vessels is extremely rare.

Keywords

segmental arterial mediolysis - dissection - aneurysm

• References

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