Abstract
A 9-year-old girl patient presented with left-sided weakness and joint contractures
developing over a period of 18 months. She was known to be suffering from β-thalassemia
major and was on regular blood transfusions. Eighteen months ago, she had suffered
from an episode of ischemic cerebrovascular accident affecting the right side of her
brain. Magnetic resonance angiogram revealed vaso-occlusive disease affecting mainly
the anterior cerebral circulation, resembling Moyamoya disease. She was advised to
carry out regular physiotherapy but her parents discontinued it, which resulted in
the gradual development of joint contractures and muscle wasting.
Keywords
thalassemia - Moyamoya syndrome - hemiplegia
