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CC BY-NC-ND 4.0 · Indian J Plast Surg 2008; 41(02): 222-225
DOI: 10.1055/s-0039-1699272
Original Article
Association of Plastic Surgeons of India

Roberts-SC syndrome, a rare syndrome and cleft palate repair

Murthy Jyotsna
Department of Plastic Surgery, Sri Ramachandra University, Porur, Chennai - 600 116, India
,
Dewan Madhu
Department of Plastic Surgery, Sri Ramachandra University, Porur, Chennai - 600 116, India
,
Hussain Altaf
Department of Plastic Surgery, Sri Ramachandra University, Porur, Chennai - 600 116, India
› Author Affiliations
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Publication History

Publication Date:
15 January 2020 (online)

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ABSTRACT

Roberts SC syndrome is a rare syndrome with only 17 previously recognized patients reported in medical literature. The syndrome is characterized by multiple malformations, particularly, symmetrical limb reduction, craniofacial anomalies such as bilateral cleft lip and palate, micrognathia, and severe growth and mental retardation. Our patient, a young child of five years having Roberts-SC, was successfully operated for cleft palate under general anesthesia. The main features of the syndrome and the technical problems of anesthesia and surgery are discussed in this report

KEY WORDS

Cleft palate - phocomelia - Roberts-SC syndrome
 
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