CC BY 4.0 · European J Pediatr Surg Rep 2019; 07(01): e63-e65
DOI: 10.1055/s-0039-1697667
Case Report
Georg Thieme Verlag KG Stuttgart · New York

Harlequin Syndrome after Thoracoscopic Repair of a Child with Tracheoesophageal Fistula (TEF)

Richard Wagner
1  Klinik und Poliklinik für Kinderchirurgie, Universitätsklinikum Leipzig, Leipzig, Sachsen, Germany
,
Martin Lacher
1  Klinik und Poliklinik für Kinderchirurgie, Universitätsklinikum Leipzig, Leipzig, Sachsen, Germany
,
Andreas Merkenschlager
2  Klinik für Neuropädiatrie, Universitätsklinikum Leipzig Klinik und Poliklinik für Kinder- und Jugendmedizin, Leipzig, Sachsen, Germany
,
Moritz Markel
1  Klinik und Poliklinik für Kinderchirurgie, Universitätsklinikum Leipzig, Leipzig, Sachsen, Germany
› Author Affiliations
Further Information

Publication History

06 August 2019

20 August 2019

Publication Date:
26 September 2019 (online)

  

Abstract

Harlequin syndrome (HS) is a rare dysautonomia of the sympathetic nervous system leading to asymmetric facial flushing and sweating. In the literature, only a few cases of HS after thoracoscopic tracheoesophageal fistula (TEF) repair are reported. We report on a newborn with TEF who developed HS after thoracoscopic repair. On the first day of life, the girl (3,480 g, gestation age: 41 week) underwent thoracoscopic repair of a type C esophageal atresia (TEF; OR time 105 minute) without complications. The postoperative course was uneventful, the patient swallowed and thrived well and did not require esophageal dilatations. At 2 years of age, missing facial flushing, transpiration, and warming on the right side of her face during agitation were noticed. As no further intervention was required, the girl and her parents adapted well to the symptoms. Our report shows that the late onset of HS after the surgical procedure is unlikely a direct causal relation to the thoracoscopic operation but rather a shared embryological pathogenesis, like a neurocristopathy.