Int J Angiol
DOI: 10.1055/s-0039-1694059
Case Report
Thieme Medical Publishers 333 Seventh Avenue, New York, NY 10001, USA.

Glomuvenous Malformation of the Neck

Muhammad Salman Khan
1  Department of Radiology, Aga Khan University, Karachi, Pakistan
Amir Humza Sohail
2  Department of Surgery, New York University Winthrop Hospital, New York, United States
Kiran Hilal
1  Department of Radiology, Aga Khan University, Karachi, Pakistan
Muhammad Hassaan Arif Maan
3  Medical College, Aga Khan University, Karachi, Pakistan
› Author Affiliations
Funding Sources There was no external financial support received for this case report.
Further Information

Publication History

Publication Date:
06 August 2019 (online)


Background The cells in glomus body regulate blood flow to the skin and play a role in temperature regulation. Glomuvenous malformations (GVMs), previously reported in literature as glomus tumors or glomangiomas, are usually present in the nail bed. In 1972, Carroll and Berman described the triad of paroxysmal stabbing pain, point tenderness, and cold hypersensitivity associated with these malformations.

Methods We present an unusual case of GVM in the neck of a 17-year-old female presenting with a painful right-sided neck mass. Physical examination revealed an approximately 2.5 × 2 cm right-sided tender neck mass; pain was exacerbated by probing with a pinhead. Computed tomography identified multiple rounded masses in the neck, with the delayed contrast filling. The patient underwent excisional biopsy of the lesion and samples were sent for histopathological examination.

Results The histopathology report, along with the radiological findings and the clinical presentation, confirmed the diagnosis of GVM. The patient remained symptom-free on long-term follow-up.

Conclusions Despite absence of previous reports, GVM can occur in neck. Surgical excision can lead to complete resolution of symptoms.