Congenital nasal glioma: a case report

Introduktion:

We present one case of a two-year old girl with congenital intranasal glioma without any intracranial extension that presented as a polyp of the nasal vestibulum.

Material and methods:

Clinical investigation and follow-up for two months. MRI of the skull. Histological work-up.

Results:

The two-year-old girl had had a polypoid mass since birth, which was located in the right vestibulum of the nose. The birth and further development of the child were without any further abnormalities. In MRI, the T1 images revealed an approx. 16 × 9 mm isointense mass in the right vestibulum with small marginal enhancement. In T2, this mass was hyperintense. In the sagittal section of the T2 images there was the assumption of a tissue bridge to the frontal dura. Intraoperatively, the polyp was firmly attached to the septum, the dome, and the lateral wall of the vestibulum, with no evidence of contact with the sinuses or towards intracranial. The excision was in toto. Histological processing revealed an encapsulated tumor with neuronal and glial tissue, which was confirmed to be glial tissue in S100 immunohistochemistry staining. The previous follow-up examinations were regular.

Conclusion:

Congenital swellings of the nose are encountered rarely, and nasal gliomas constitute about 5% of such lesions. Various theories have been suggested to explain the pathogenesis. Imaging preferably by MRI is important to study the extent and to rule out intracranial extension. Treatment of choise is complete excision, and the approach depends upon the extent of the lesion and availability of expertise.

Publication History

Publication Date:
23 April 2019 (online)