Case report: 53-year-old female patient with progressive combined deafness and facial palsy as part of a hemangiopericytoma in the petrous bone and middle cranial fossa

Introduction:

Hemangiopericytomas are malignant vascular tumors originated from pericytes. They are characterized by a slow, repressive growth, whereby their symptoms can be diverse. The classical origin localization concerns the lower extremity as well as the retroperitoneal space, only rarely these are found in the area of the CNS.

Case:

We report a 53-year-old female patient presenting with subacute hearing loss. There was a known chronic peripheral facial palsy.

Results:

The clinical examination revealed a peripheral facial paralysis of the House Brackman Score VI. The ear microscopy showed an intact and reddened eardrum on the right side. Pure tone audiometry showed a combined hearing loss of 50 dB at 2 kHz to a maximum of 80 dB at 1 kHz with an air-bone gap of 20 – 30 dB and normal hearing on the left. Biopsy results showed a hemangiopericytoma. CT morphologically, the picture consisted of a mass in the right petrous bone with contact to the inner ear canal and tumorous cochlear and labyrinth. There was an interdisciplinary resection with the colleagues of neurosurgery performing a translab- and middle fossa approach.

Discussion:

In the context of our case report we discuss the diagnostic and therapeutic options of this hemangiopericytoma manifestation.

Publication History

Publication Date:
23 April 2019 (online)