The Rare Case of Anti-VGKC Limbic Encephalitis Secondary to High-Grade Glioma
30 August 2018
09 January 2019
21 February 2019 (eFirst)
Introduction Paraneoplastic limbic encephalitis secondary to a glial tumor is rare, and limited reports on this occurrence have been made in the pediatric population.
Case Report This case involves a 13-year-old female patient with anti-voltage gated potassium channel (anti-VGKC) limbic encephalitis secondary to a high-grade glioma (HGG) in the suprasellar region.
Discussion HHGs, associated with anti-VGKC antibodies, are a rare occurrence. This case highlights the need for the inclusion of glial neoplasms in the differential diagnosis for patients presenting with symptoms associated with paraneoplastic encephalitis.
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