Abstract
Noncompaction cardiomyopathy (NCCM) and left ventricular noncompaction (LVNC), in
their isolated form, are rare cardiomyopathies. They are characterized by a thickened
myocardium due to the presence of deep trabeculae recesses, and to thick trabeculae.
This condition is associated with a variable clinical phenotype including heart failure,
thromboembolism, and sudden death. We report a case of LVNC at 26 weeks and 4 days
of gestation revised on the basis of what is currently reported in the literature.
A review of the literature was performed to better describe this rare condition. Left
ventricular noncompaction is a rare fetal condition and it should be suspected in
case of cardiomyopathy.
Keywords
noncompaction cardiomyopathy - spongy myocardium - left ventricular noncompaction
cardiomyopathy
