Neuropediatrics 2018; 49(06): 405-407
DOI: 10.1055/s-0038-1669923
Short Communication
Georg Thieme Verlag KG Stuttgart · New York

Isolated Congenital Absence of Cranial Nerves: Report of Two Cases

Vivek Agarwal
1   Department of Radiodiagnosis and Pediatric Neurology, PGIMER, Chandigarh, Punjab, India
,
Sameer Vyas
1   Department of Radiodiagnosis and Pediatric Neurology, PGIMER, Chandigarh, Punjab, India
,
Sumeet R. Dhawan*
1   Department of Radiodiagnosis and Pediatric Neurology, PGIMER, Chandigarh, Punjab, India
,
Naveen Sankhyan*
1   Department of Radiodiagnosis and Pediatric Neurology, PGIMER, Chandigarh, Punjab, India
› Author Affiliations
Further Information

Publication History

24 June 2018

31 July 2018

Publication Date:
10 September 2018 (online)

Abstract

Isolated cranial nerve absence is a rare condition that can be diagnosed using high-resolution cranial nerve magnetic resonance (MR) imaging. Thorough clinical examination with proper knowledge of the course of cranial nerves may help diagnose this rare condition. We describe two cases, one each of, isolated congenital absence of the third and seventh cranial nerve with their clinical presentation. High-resolution T2-weighted MR imaging was done in both patients which revealed absence of cisternal segment of the right-sided third nerve and cisternal with canalicular segment of the right-sided facial nerve.

* These authors contributed equally to the manuscript.


 
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