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DOI: 10.1055/s-0038-1666965
Role of Preoperative Embolization for Hypervascular Cherubism
Publication History
Received: 06 April 2018
Accepted: 24 May 2018
Publication Date:
31 July 2018 (online)
Cherubism is an autosomal dominant condition, first described by Jones in three siblings who presented with a fullness of the cheeks and enlargement of the jaws.[1] The characteristic appearance closely resembled the Renaissance cherubs inspiring Jones to name it as cherubism.[2] [3] The condition is a fibro-osseous dysplasia characterized by painless symmetrical enlargement of the jaws. The mean age at the time of presentation is 7 years with a range of 12 months to 14 years.[4] The condition has a 100% penetrance in males and 50 to 70% in females.[5] In this article, we describe the role of angiography and embolization for a rare hypervascular variant of cherubism prior to surgical therapy.
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