CC BY-NC-ND 4.0 · Journal of Clinical Interventional Radiology ISVIR 2018; 02(02): 121-125
DOI: 10.1055/s-0038-1666965
Letter to the Editor
Thieme Medical and Scientific Publishers Private Ltd.

Role of Preoperative Embolization for Hypervascular Cherubism

Soumil Singhal
1   Department of Intervention Radiology and Intervention Oncology, BGS Gleneagles Global Hospital, Bangalore, Karnataka, India
,
Rohit Madhurkar
1   Department of Intervention Radiology and Intervention Oncology, BGS Gleneagles Global Hospital, Bangalore, Karnataka, India
,
Krishna Shama Rao
2   Department of Craniofacial Surgery, BGS Gleneagles Global Hospital, Bangalore, Karnataka, India
,
Bibin Sebastian
1   Department of Intervention Radiology and Intervention Oncology, BGS Gleneagles Global Hospital, Bangalore, Karnataka, India
,
M. C. Uthappa
1   Department of Intervention Radiology and Intervention Oncology, BGS Gleneagles Global Hospital, Bangalore, Karnataka, India
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Weitere Informationen

Publikationsverlauf

Received: 06. April 2018

Accepted: 24. Mai 2018

Publikationsdatum:
31. Juli 2018 (online)

Cherubism is an autosomal dominant condition, first described by Jones in three siblings who presented with a fullness of the cheeks and enlargement of the jaws.[1] The characteristic appearance closely resembled the Renaissance cherubs inspiring Jones to name it as cherubism.[2] [3] The condition is a fibro-osseous dysplasia characterized by painless symmetrical enlargement of the jaws. The mean age at the time of presentation is 7 years with a range of 12 months to 14 years.[4] The condition has a 100% penetrance in males and 50 to 70% in females.[5] In this article, we describe the role of angiography and embolization for a rare hypervascular variant of cherubism prior to surgical therapy.