Thromb Haemost 1972; 28(03): 489-495
DOI: 10.1055/s-0038-1649033
Original Article
Schattauer GmbH

Variants of Haemophilia B

Susan Elödi
1   Laboratory of Blood Coagulation and Department of Immunochemistry, Central Institute of Haematology and Blood Transfusion, Budapest, Hungary
,
Éva Puskás
1   Laboratory of Blood Coagulation and Department of Immunochemistry, Central Institute of Haematology and Blood Transfusion, Budapest, Hungary
› Author Affiliations
Further Information

Publication History

Publication Date:
29 June 2018 (online)

Summary

Variants of haemophilia B were examined by antibody-neutralization technique and by the ox brain thromboplastin time method. On the basis of the presence or absence of anomalous factor IX and of prothrombin time, four variants of haemophilia B were discerned. It is shown that the prolongation of prothrombin time, measured in our cases, cannot be attributed to an inhibitor in the patients’ plasma.

 
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