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Thromb Haemost 1974; 32(02/03): 538-548
DOI: 10.1055/s-0038-1647722
DOI: 10.1055/s-0038-1647722
Original Article
Severe Factor V Deficiency with Prolonged Bleeding Time
Weitere Informationen
Publikationsverlauf
Received
12. Juni 1974
Accepted
11. Juli 1974
Publikationsdatum:
30. Juni 2018 (online)
Summary
A patient with two congenital defects, i.e. a severe factor V deficiency and an aortic coarctation is described. Arguments for a dominant mode of inheritance of the factor V deficiency are presented. A coinciding haemostatic defect consisting of a prolonged bleeding time, which could be corrected by fresh plasma and cryoprecipitate, and a decreased platelet retention in the glass bead test disappeared after surgical correction of the coarctation.
Extensive platelet studies failed to show any further defect.
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