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J Neurol Surg A Cent Eur Neurosurg 2018; 79(06): 541-549
DOI: 10.1055/s-0038-1641178
Case Report
Georg Thieme Verlag KG Stuttgart · New York

Congenital Arteriovenous Malformation of the Scalp Involving the Orbit

Alberto Feletti
1   Department of Neurosurgery, Azienda Ospedaliero-Universitaria di Modena, Via Giardini 1355, 41121 Modena, Italy
,
Stavros Dimitriadis
1   Department of Neurosurgery, Azienda Ospedaliero-Universitaria di Modena, Via Giardini 1355, 41121 Modena, Italy
,
Stefano Vallone
2   Department of Neuroradiology, Azienda Ospedaliero-Universitaria di Modena, Modena, Italy
,
Giacomo Pavesi
1   Department of Neurosurgery, Azienda Ospedaliero-Universitaria di Modena, Via Giardini 1355, 41121 Modena, Italy
› Author Affiliations
Further Information

Publication History

17 August 2017

08 February 2018

Publication Date:
15 June 2018 (online)

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Abstract

Background Arteriovenous malformations (AVMs) of the scalp are rare and infrequently encountered by the neurosurgeon.

Case Description We report a unique case of a 42-year-old patient who presented with a progressive worsening of visual acuity in the right eye (lower quadrantanopia) and palpebral ptosis. Physical examination revealed a right exophthalmos and a right frontoparietal scalp soft swelling when the patient was in the supine position. Neurologic work-up showed a scalp AVM extending into the orbit and connected to an intraorbital cavernous angioma. The patient was treated with a frontotemporal craniotomy and decompression of the orbit.

Conclusions In the rare case of intraorbital extension of a scalp AVM, neurologic symptoms may appear when the size of the vascular malformation increases with age. The aims of surgery should be decompression of the orbit and aesthetic preservation, rather than complete excision. A review of the literature is also provided.

Keywords

arteriovenous malformation - cavernous angioma - cirsoid aneurysm - intraorbital - scalp
 

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