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CC BY-NC-ND 4.0 · AJP Rep 2018; 08(01): e1-e3
DOI: 10.1055/s-0037-1615818
Case Report
Thieme Medical Publishers 333 Seventh Avenue, New York, NY 10001, USA.

Myelomeningocele with Unilateral Right Renal Agenesis: A Case Report

Hajime Maeda
1   Department of Pediatrics, Fukushima Medical University School of Medicine, Fukushima, Fukushima, Japan
,
Hayato Go
1   Department of Pediatrics, Fukushima Medical University School of Medicine, Fukushima, Fukushima, Japan
,
Jun Sakuma
2   Department of Neurosurgery, Fukushima Medical University School of Medicine, Fukushima, Fukushima, Japan
,
Takashi Imamura
1   Department of Pediatrics, Fukushima Medical University School of Medicine, Fukushima, Fukushima, Japan
,
Maki Sato
1   Department of Pediatrics, Fukushima Medical University School of Medicine, Fukushima, Fukushima, Japan
,
Nobuo Momoi
1   Department of Pediatrics, Fukushima Medical University School of Medicine, Fukushima, Fukushima, Japan
,
Mitsuaki Hosoya
1   Department of Pediatrics, Fukushima Medical University School of Medicine, Fukushima, Fukushima, Japan
› Institutsangaben
Weitere Informationen

Publikationsverlauf

29. September 2017

19. November 2017

Publikationsdatum:
09. Januar 2018 (online)

   Lizenzen und Reprints

Abstract

Congenital anomalies of the spine may occur with malformations of the central nervous, cardiovascular, gastrointestinal, respiratory, and genitourinary systems. This is a case of myelomeningocele with unilateral right renal agenesis in a newborn. The patient suffered complications of cerebrospinal fluid leak and meningitis, but was successfully treated and discharged on day 86. In this case, unilateral right renal agenesis represented a significant surgical risk because failure of the remaining kidney could result in renal failure. Because congenital anomalies of the spine may be associated with malformations of the genitourinary system, and additional surgeries were necessary in our case following birth, it is very important that the presence of genitourinary malformations be evaluated.

Keywords

Chiari malformation - congenital anomalies - genitourinary system - myelomeningocele - neural tube defects
 

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