CC BY-NC-ND 4.0 · Int Arch Otorhinolaryngol 2017; 21(02): 195-198
DOI: 10.1055/s-0037-1599785
Systematic Review – The Surgical Management of Vestibular Disorders
Thieme-Revinter Publicações Ltda Rio de Janeiro, Brazil

Superior Semicircular Canal Dehiscence Syndrome – Diagnosis and Surgical Management

Marite Palma Diaz
1   Otorhinolaryngology and Neurotology Department, Instituto Nacional de Neurología y Neurocirugía Dr. Manuel Velasco Suárez, México, DF, Mexico
2   Neurology Center, Centro Médico American British Cowdray, México, DF, Mexico
,
Juan Carlos Cisneros Lesser
3   Otorhinolaryngology and Neurotology Depaertment, Instituto Nacional de Rehabilitación, México, DF, Mexico
,
Alfredo Vega Alarcón
1   Otorhinolaryngology and Neurotology Department, Instituto Nacional de Neurología y Neurocirugía Dr. Manuel Velasco Suárez, México, DF, Mexico
2   Neurology Center, Centro Médico American British Cowdray, México, DF, Mexico
› Author Affiliations
Further Information

Publication History

02 December 2016

01 February 2017

Publication Date:
31 March 2017 (online)

Abstract

Introduction Superior semicircular canal dehiscence syndrome was described by Minor et al in 1998. It is a troublesome syndrome that results in vertigo and oscillopsia induced by loud sounds or changes in the pressure of the external auditory canal or middle ear. Patients may present with autophony, hyperacusis, pulsatile tinnitus and hearing loss. When symptoms are mild, they are usually managed conservatively, but surgical intervention may be needed for patients with debilitating symptoms.

Objective The aim of this manuscript is to review the different surgical techniques used to repair the superior semicircular canal dehiscence.

Data Sources PubMed and Ovid-SP databases.

Data Synthesis The different approaches are described and discussed, as well as their limitations. We also review the advantages and disadvantages of the plugging, capping and resurfacing techniques to repair the dehiscence.

Conclusions Each of the surgical approaches has advantages and disadvantages. The middle fossa approach gives a better view of the dehiscence, but comes with a higher morbidity than the transmastoid approach. Endoscopic assistance may be advantageous during the middle cranial fossa approach for better visualization. The plugging and capping techniques are associated with higher success rates than resurfacing, with no added risk of hearing loss.

 
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