CC BY 4.0 · European J Pediatr Surg Rep. 2017; 05(01): e1-e3
DOI: 10.1055/s-0037-1598624
Case Report
Georg Thieme Verlag KG Stuttgart · New York

Discontinued Splenogonadal Fusion and Bilateral Empty Scrotum in an 18-Month-Old Boy

Ahmed Abokrecha
1   Department of Pediatric Surgery, Maternity and Children Hospital, Makkah, Saudi Arabia
Ameera Almatrfi
2   Department of Medicine and Surgery, Umm Al-Qura University Faculty of Medicine, Makkah, Saudi Arabia
› Author Affiliations
Further Information

Publication History

16 August 2016

05 January 2017

Publication Date:
02 March 2017 (online)


Splenogonadal fusion is a rare benign congenital anomaly defined as the presence of splenic tissue adherent to gonads. It was first described in 1883 by Bostroem, a German pathologist. We present a case of an 18-month-old boy who was referred as a case of bilateral empty scrotum since birth. During routine laparoscopic exploration, right vas deferens and testicular vessels were entering the right internal inguinal ring so right inguinal exploration was done, which revealed blind ending vas deferens and testicular vessels and the left testis was found intra-abdominally near the left internal ring with a mass on its upper pole. Wedge biopsy was taken from the upper pole of the testicle (site of the mass) for tissue diagnosis followed by orchidopexy. Histology showed splenic tissue. Although splenogonadal fusion is a rare condition, surgeons should be aware of this rare disease entity to avoid unnecessary aggressive interventions such as orchiectomy.

  • References

  • 1 Shadpour P, Rezaimehr B. “Rosary of Testes”: splenogonadal fusion in association with bilateral abdominal testes presenting as polyorchidism. Case Rep Urol 2015; 2015: 317189
  • 2 Celik A, Tiryaki S, Darcan S, Ergun O. Splenogonadal fusion-limb deformity syndrome: a rare but important cause of undescended testis. World J Pediatr 2016; 12 (02) 246-248
  • 3 Bosnalı O, Cici İ, Moralıoğlu S, Cerrah-Celayir A. Continuous-type splenogonadal fusion: report of a rare case. Turk J Pediatr 2014; 56 (06) 680-683
  • 4 Melikov R, Altunkol A, Quliyev F, Mammadov E, Abat D. Continuous-type splenogonadal fusion: a rare cause of scrotal swelling. Pediatr Urol Case Rep 2015; 2 (02) 22
  • 5 Lakshmanan PM, Reddy AK, Nutakki A. A surprising content of congenital hernia: complete splenogonadal fusion band. BMJ Case Rep 2014; 2014 (14) :pii: bcr2014203640
  • 6 Kennedy KP, Barnard S, Speakman MJ. Splenogonadal fusion - not just another hydrocoele. Ann R Coll Surg Engl 2006; 88 (02) 163-164
  • 7 Ferrón SA, Arce JD. Discontinuous splenogonadal fusion: new sonographic findings. Pediatr Radiol 2013; 43 (12) 1652-1655
  • 8 Milliken I, Cherian A, Najmaldin A, Powis MR. Splenogonadal fusion: a rare cause of testicular enlargement. Pediatr Surg Int 2007; 23 (04) 365-367
  • 9 Chen SL, Kao YL, Sun HS, Lin WL. Splenogonadal fusion. J Formos Med Assoc 2008; 107 (11) 892-895
  • 10 Imperial SL, Sidhu JS. Nonseminomatous germ cell tumor arising in splenogonadal fusion. Arch Pathol Lab Med 2002; 126 (10) 1222-1225
  • 11 Hasegawa Y, Kanemitsu I, Ueoka K. Transverse testicular ectopia with splenogonadal fusion: a case report. Int J Urol 2011; 18 (06) 466-468
  • 12 Zhang X-w, Hou G-j, Geng X-j, Gao X-y, Chen Y-j, Fu L-b. Splenogonadal fusion: Report of two cases and literature review. J Pediatr Surg Case Rep 2013; 1 (10) 362-363
  • 13 Li WF, Luan MX, Ma Z, Chen YJ. Splenogonadal fusion: report of four cases and review of the literature. Exp Ther Med 2013; 6 (03) 816-818