AJP Rep 2016; 06(03): e260-e263
DOI: 10.1055/s-0036-1585578
Case Report
Thieme Medical Publishers 333 Seventh Avenue, New York, NY 10001, USA.

Infantile Hepatic Hemangioendothelioma: An Uncommon Cause of Persistent Pulmonary Hypertension in a Newborn Infant

Trassanee Chatmethakul
1  Department of Pediatrics, University of South Alabama, Mobile, Alabama
,
Ramachandra Bhat
1  Department of Pediatrics, University of South Alabama, Mobile, Alabama
,
Maryam Alkaabi
1  Department of Pediatrics, University of South Alabama, Mobile, Alabama
,
Abdul Siddiqui
1  Department of Pediatrics, University of South Alabama, Mobile, Alabama
,
Keith Peevy
1  Department of Pediatrics, University of South Alabama, Mobile, Alabama
,
Michael Zayek
1  Department of Pediatrics, University of South Alabama, Mobile, Alabama
› Author Affiliations
Further Information

Publication History

01 February 2016

31 May 2016

Publication Date:
22 July 2016 (online)

  

Abstract

Multifocal and diffuse infantile hepatic hemangioendotheliomas commonly present with signs of high-output congestive heart failure. In addition, prolonged persistent pulmonary overcirculation eventually leads to the development of pulmonary hypertension at a later age. We report a 2-day old, full-term infant with multifocal, large infantile hepatic hemangioendothelioma, who presented with an early onset of pulmonary hypertension, managed successfully with supportive care and systemic therapy directed toward the involution of infantile hepatic hemangioendothelioma.