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AJP Rep 2016; 06(02): e246-e249
DOI: 10.1055/s-0036-1584530
Case Report
Thieme Medical Publishers 333 Seventh Avenue, New York, NY 10001, USA.

Bilateral Pulmonary Agenesis: A Rare and Unexpected Finding in a Newborn

Lananh N. Nguyen
1   Department of Pathology, Dartmouth-Hitchcock Medical Center, Lebanon, New Hampshire
,
W. Tony Parks
2   Departments of Pathology and Obstetrics, Gynecology and Reproductive Sciences, Magee Women's Hospital, University of Pittsburgh School of Medicine, Pittsburgh, Pennsylvania
› Author Affiliations
Further Information

Publication History

29 March 2016

06 May 2016

Publication Date:
29 June 2016 (online)

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Abstract

Background Bilateral pulmonary agenesis is a rare congenital anomaly incompatible with life that can be missed on routine prenatal screening. Prenatal ultrasound diagnosis of this fatal anomaly can aid in prenatal counseling and postdelivery care.

Case Study We report the case of a newborn who was born prematurely at 29 weeks gestation and underwent several unsuccessful intubation attempts immediately after delivery.

Conclusion Autopsy examination revealed bilateral pulmonary agenesis with a short, blindly ending trachea.

Keywords

bilateral pulmonary agenesis - lung anomaly - developmental anomaly
 

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