Rare Etiology of Cardiogenic Shock in Children: Anomalous Origin of the Left Coronary Artery from the Opposite Sinus with an Intramural Course

Abstract

Anomalous origin of the left coronary artery from the right sinus of Valsalva with an intramural course is a rare but potentially lethal congenital defect. While anomalous origin of the left coronary artery is a well-known cause of sudden cardiac death, it is less well appreciated that this anomaly may manifest in a variety of other clinical presentations, thereby leaving these patients at risk of missed or delayed diagnosis and subsequent poor outcomes. In this report, we describe an adolescent male with an unusual etiology of cardiogenic shock.

Keywords

congenital coronary artery anomaly - presentation - diagnosis

• References

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