Congenital Seminal Vesicle Cyst and Ipsilateral Renal Agenesis (Zinner Syndrome): A Rare Association and Its Evolution from Early Childhood to Adolescence

Abstract

Zinner syndrome, the association of congenital seminal vesicle cyst and ipsilateral renal agenesis, is more often reported in adults or older adolescents. We present a case of a boy, followed up in our hospital since birth for right renal agenesis who at the age of 4 years presented a right paravesical cyst on ultrasound. The cyst was initially considered as an ureterocele. The diagnosis of Zinner syndrome was made later, at the age of 15 years by ultrasound and magnetic resonance imaging; at that moment the cyst had increased in size and had changed in aspect. This malformation should be considered in the differential diagnosis of a pelvic cyst in male patients with renal agenesis.

Keywords

seminal vesicle - cyst - renal agenesis - Zinner syndrome

• References

• 1 Kao CC, Wu CJ, Sun GH , et al. Congenital seminal vesicle cyst associated with ipsilateral renal agenesis mimicking bladder outlet obstruction: a case report and review of the literature. Kaohsiung J Med Sci 2010; 26 (1) 30-34
• 2 Livingston L, Larsen CR. Seminal vesicle cyst with ipsilateral renal agenesis. AJR Am J Roentgenol 2000; 175 (1) 177-180
• 3 Pace G, Galatioto GP, Gualà L, Ranieri G, Vicentini C. Ejaculatory duct obstruction caused by a right giant seminal vesicle with an ipsilateral upper urinary tract agenesia: an embryologic malformation. Fertil Steril 2008; 89 (2) 390-394
• 4 Pereira BJ, Sousa L, Azinhais P , et al. Zinner's syndrome: an up-to-date review of the literature based on a clinical case. Andrologia 2009; 41 (5) 322-330
• 5 Ghonge NP, Aggarwal B, Sahu AK. Zinner syndrome: A unique triad of mesonephric duct abnormalities as an unusual cause of urinary symptoms in late adolescence. Indian J Urol 2010; 26 (3) 444-447
• 6 Sundar R, Sundar G. Zinner syndrome: an uncommon cause of painful ejaculation. BMJ Case Rep 2015; 2015 (15) xx
• 7 Cherullo EE, Meraney AM, Bernstein LH, Einstein DM, Thomas AJ, Gill IS. Laparoscopic management of congenital seminal vesicle cysts associated with ipsilateral renal agenesis. J Urol 2002; 167 (3) 1263-1267
• 8 Liatsikos EN, Lee B, Filos KS, Barbalias GA. Congenital seminal vesicle cyst and coexisting renal agenesis: laparoscopic approach. Urology 2004; 63 (3) 584-586
• 9 Seo IY, Kim HS, Rim JS. Congenital seminal vesicle cyst associated with ipsilateral renal agenesis. Yonsei Med J 2009; 50 (4) 560-563
• 10 van den Ouden D, Blom JH, Bangma C, de Spiegeleer AH. Diagnosis and management of seminal vesicle cysts associated with ipsilateral renal agenesis: a pooled analysis of 52 cases. Eur Urol 1998; 33 (5) 433-440
• 11 Jarzemski P, Listopadzki S, Kowalski M. Laparoscopic removal of a congenital seminal vesicle cyst in Zinner's syndrome. JSLS 2014; 18 (2) 367-371
• 12 Basillote JB, Shanberg AM, Woo D, Perer E, Rajpoot D, Clayman RV. Laparoscopic excision of a seminal vesicle cyst in a child. J Urol 2004; 171 (1) 369-371
• 13 Valla JS, Carfagna L, Tursini S, Mohaidi MA, Bosson N, Steyaert H. Congenital seminal vesicle cyst: prenatal diagnosis and postnatal laparoscopic excision with an attempt to preserve fertility. BJU Int 2003; 91 (9) 891-892