Relapsing–Remitting Encephalopathy with Status Epilepticus: Think Hashimoto Encephalopathy

Abstract

Hashimoto encephalopathy is a rare syndrome in children with nonspecific clinical symptoms, which leads to underdiagnosis. Encephalopathy with a high thyroperoxidase antibody levels and exclusion of other causes can provide a diagnosis unrelated to thyroid hormone status. An acute, subacute, chronic, progressive, or relapsing–remitting course can be seen. The main therapy for Hashimoto encephalopathy is steroid administration, which lends its other name as steroid-responsive encephalopathy associated with autoimmune thyroiditis. However, there are few cases with spontaneous remission without steroid therapy. Here, we report a case with a relapsing course but spontaneous remission.

Keywords

Hashimoto encephalopathy - status epilepticus - children - recurrent encephalopathy

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