Journal of Pediatric Epilepsy 2015; 04(02): 080-084
DOI: 10.1055/s-0035-1555598
Case Report
Georg Thieme Verlag KG Stuttgart · New York

Relapsing–Remitting Encephalopathy with Status Epilepticus: Think Hashimoto Encephalopathy

Serdal Güngör
1   Department of Pediatric Neurology, Faculty of Medicine, İnönü University, Malatya, Turkey
,
Sabiha G. Raif
1   Department of Pediatric Neurology, Faculty of Medicine, İnönü University, Malatya, Turkey
› Author Affiliations
Further Information

Publication History

08 December 2013

06 September 2014

Publication Date:
31 July 2015 (online)

Abstract

Hashimoto encephalopathy is a rare syndrome in children with nonspecific clinical symptoms, which leads to underdiagnosis. Encephalopathy with a high thyroperoxidase antibody levels and exclusion of other causes can provide a diagnosis unrelated to thyroid hormone status. An acute, subacute, chronic, progressive, or relapsing–remitting course can be seen. The main therapy for Hashimoto encephalopathy is steroid administration, which lends its other name as steroid-responsive encephalopathy associated with autoimmune thyroiditis. However, there are few cases with spontaneous remission without steroid therapy. Here, we report a case with a relapsing course but spontaneous remission.