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AJP Rep 2015; 05(02): e161-e164
DOI: 10.1055/s-0035-1554799
Case Report
Thieme Medical Publishers 333 Seventh Avenue, New York, NY 10001, USA.

Multimodality Renal Failure in a Patient with OEIS Complex

Jonathan D. Santoro
1   Department of Pediatrics, Stanford University School of Medicine, Palo Alto, California
,
Stephanie Chao
2   Department of Surgery, Stanford University School of Medicine, Palo Alto, California
,
Michael H. Hsieh
3   Department of Urology, Children's National Health System, Washington, District of Columbia
,
Henry C. Lee
4   Division of Neonatology, Department of Pediatrics, Stanford University School of Medicine, Palo Alto, California
› Author Affiliations
Further Information

Publication History

27 January 2015

20 April 2015

Publication Date:
12 June 2015 (online)

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Abstract

Omphalocele-exstrophy of the bladder-imperforate anus-spinal defect (OEIS) complex is a rare constellation of clinical abnormalities with wide phenotypic presentation. We describe a case of a preterm neonate with OEIS complex with acute renal failure, and the challenges in diagnosis and management of this patient as renal failure can be a multifactorial process when encountered with this rare complex.

Keywords

OEIS - renal injury - genitourinary - obstructive nephropathy
 

  • References

  • 1 Carey JC, Greenbaum B, Hall BD. The OEIS complex (omphalocele, exstrophy, imperforate anus, spinal defects). Birth Defects Orig Artic Ser 1978; 14 (6B) 253-263
    PubMedGoogle Scholar
  • 2 Feldkamp ML, Botto LD, Amar E , et al. Cloacal exstrophy: an epidemiologic study from the International Clearinghouse for Birth Defects Surveillance and Research. Am J Med Genet C Semin Med Genet 2011; 157C (4) 333-343
    PubMedGoogle Scholar
  • 3 Hurwitz RS, Manzoni GA, Ransley PG, Stephens FD. Cloacal exstrophy: a report of 34 cases. J Urol 1987; 138 (4 Pt 2) 1060-1064
    PubMedGoogle Scholar
  • 4 Muecke EC. The role of the cloacal membrane in extrosphy: the first successful experimental study. J Urol 1964; 92: 659-667
    PubMedGoogle Scholar
  • 5 Phillips TM, Salmasi AH, Stec A, Novak TE, Gearhart JP, Mathews RI. Urological outcomes in the omphalocele exstrophy imperforate anus spinal defects (OEIS) complex: experience with 80 patients. J Pediatr Urol 2013; 9 (3) 353-358
    CrossrefPubMedGoogle Scholar
  • 6 Mukherjee B, McCauley E, Hanford RB, Aalsma M, Anderson AM. Psychopathology, psychosocial, gender and cognitive outcomes in patients with cloacal exstrophy. J Urol 2007; 178 (2) 630-635 , discussion 634–635
    CrossrefPubMedGoogle Scholar
  • 7 Duhamel B. Embryology of exomphalos and allied malformations. Arch Dis Child 1963; 38 (198) 142-147
    CrossrefPubMedGoogle Scholar
  • 8 van der Putte SCJ, Spliet WGM, Nikkels PG. Common (“classical”) and covered cloacal exstrophy: a histopathological study and a reconstruction of the pathogenesis. Pediatr Dev Pathol 2008; 11 (6) 430-442
    CrossrefPubMedGoogle Scholar
  • 9 Hong R, Lim SC, Jang JW , et al. OEIS complex with glomerulocystic kidney disease: a case report. Pediatr Dev Pathol 2007; 10 (2) 121-124
    CrossrefPubMedGoogle Scholar
  • 10 McCune TR, Stone WJ, Breyer JA. Page kidney: case report and review of the literature. Am J Kidney Dis 1991; 18 (5) 593-599
    CrossrefPubMedGoogle Scholar