Clinical Characteristics of Posterior and Lateral Semicircular Canal Dehiscence

Marko Spasic; Andy Trang; Lawrance K. Chung; Nolan Ung; Kimberly Thill; Golmah Zarinkhou; Quinton S. Gopen; Isaac Yang

doi:10.1055/s-0035-1551667

Journal of Neurological Surgery Part B: Skull Base, Table of Contents

J Neurol Surg B Skull Base 2015; 76(06): 421-425
DOI: 10.1055/s-0035-1551667

Original Article

Georg Thieme Verlag KG Stuttgart · New York

Clinical Characteristics of Posterior and Lateral Semicircular Canal Dehiscence

Authors

Marko Spasic

¹Department of Neurosurgery, University of California, Los Angeles, Los Angeles, California, United States
Andy Trang

¹Department of Neurosurgery, University of California, Los Angeles, Los Angeles, California, United States
Lawrance K. Chung

¹Department of Neurosurgery, University of California, Los Angeles, Los Angeles, California, United States
Nolan Ung

¹Department of Neurosurgery, University of California, Los Angeles, Los Angeles, California, United States
Kimberly Thill

¹Department of Neurosurgery, University of California, Los Angeles, Los Angeles, California, United States
Golmah Zarinkhou

¹Department of Neurosurgery, University of California, Los Angeles, Los Angeles, California, United States
Quinton S. Gopen

²Division of Otolaryngology Head and Neck Surgery, University of California, Los Angeles, Los Angeles, California, United States
Isaac Yang

¹Department of Neurosurgery, University of California, Los Angeles, Los Angeles, California, United States

³UCLA Jonsson Comprehensive Cancer Center, University of California, Los Angeles, Los Angeles, California, United States

Abstract

The objective of this study was to evaluate the characteristic symptoms of and treatments for lateral semicircular canal dehiscence (LSCD) and posterior semicircular canal dehiscence (PSCD) and its proposed mechanism. A dehiscence acquired in any of the semicircular canals may evoke various auditory symptoms (autophony and inner ear conductive hearing loss) or vestibular symptoms (vertigo, the Tullio phenomenon, and Hennebert sign) by creating a “third mobile window” in the bone that enables aberrant communication between the inner ear and nearby structures. A PubMed search was performed using the keywords lateral, posterior, and semicircular canal dehiscence to identify all relevant cases. Our data suggest that PSCD, although clinically rare, is most likely associated with a high-riding jugular bulb and fibrous dysplasia. Patients may experience auditory manifestations that range from mild conductive to extensive sensorineural hearing loss. LSCD is usually associated with chronic otitis media with cholesteatoma.

Keywords

posterior semicircular canal dehiscence syndrome - lateral semicircular canal dehiscence syndrome - superior semicircular canal dehiscence syndrome - vertigo - autophony

Full Text

References

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