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J Neurol Surg B Skull Base 2015; 76(06): 421-425
DOI: 10.1055/s-0035-1551667
Original Article
Georg Thieme Verlag KG Stuttgart · New York

Clinical Characteristics of Posterior and Lateral Semicircular Canal Dehiscence

Marko Spasic
1   Department of Neurosurgery, University of California, Los Angeles, Los Angeles, California, United States
,
Andy Trang
1   Department of Neurosurgery, University of California, Los Angeles, Los Angeles, California, United States
,
Lawrance K. Chung
1   Department of Neurosurgery, University of California, Los Angeles, Los Angeles, California, United States
,
Nolan Ung
1   Department of Neurosurgery, University of California, Los Angeles, Los Angeles, California, United States
,
Kimberly Thill
1   Department of Neurosurgery, University of California, Los Angeles, Los Angeles, California, United States
,
Golmah Zarinkhou
1   Department of Neurosurgery, University of California, Los Angeles, Los Angeles, California, United States
,
Quinton S. Gopen
2   Division of Otolaryngology Head and Neck Surgery, University of California, Los Angeles, Los Angeles, California, United States
,
Isaac Yang
1   Department of Neurosurgery, University of California, Los Angeles, Los Angeles, California, United States
3   UCLA Jonsson Comprehensive Cancer Center, University of California, Los Angeles, Los Angeles, California, United States
› Author Affiliations
Further Information

Publication History

06 June 2014

08 March 2015

Publication Date:
29 May 2015 (online)

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Abstract

The objective of this study was to evaluate the characteristic symptoms of and treatments for lateral semicircular canal dehiscence (LSCD) and posterior semicircular canal dehiscence (PSCD) and its proposed mechanism. A dehiscence acquired in any of the semicircular canals may evoke various auditory symptoms (autophony and inner ear conductive hearing loss) or vestibular symptoms (vertigo, the Tullio phenomenon, and Hennebert sign) by creating a “third mobile window” in the bone that enables aberrant communication between the inner ear and nearby structures. A PubMed search was performed using the keywords lateral, posterior, and semicircular canal dehiscence to identify all relevant cases. Our data suggest that PSCD, although clinically rare, is most likely associated with a high-riding jugular bulb and fibrous dysplasia. Patients may experience auditory manifestations that range from mild conductive to extensive sensorineural hearing loss. LSCD is usually associated with chronic otitis media with cholesteatoma.

Keywords

posterior semicircular canal dehiscence syndrome - lateral semicircular canal dehiscence syndrome - superior semicircular canal dehiscence syndrome - vertigo - autophony
 

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