Int Arch Otorhinolaryngol 2015; 19(04): 349-353
DOI: 10.1055/s-0034-1396793
Case Report
Thieme Publicações Ltda Rio de Janeiro, Brazil

Massive Plexiform Neurofibroma of the Neck and Larynx

Mohammad Kamal Mobashir
1  Department of Otorhinolaryngology-Head and Neck Surgery, Zagazig University, Zagazig, Egypt
,
Abd ElRaof Said Mohamed
1  Department of Otorhinolaryngology-Head and Neck Surgery, Zagazig University, Zagazig, Egypt
,
Mohammad Waheed El-Anwar
1  Department of Otorhinolaryngology-Head and Neck Surgery, Zagazig University, Zagazig, Egypt
,
Ahmad Ebrahim El Sayed
1  Department of Otorhinolaryngology-Head and Neck Surgery, Zagazig University, Zagazig, Egypt
,
Mouhamad A. Fouad
2  Department of Pathology, Zagazig University, Zagazig, Egypt
› Author Affiliations
Further Information

Publication History

22 October 2014

10 November 2014

Publication Date:
12 December 2014 (online)

  

Abstract

Introduction Laryngeal neurofibromas are extremely rare, accounting for only 0.03 to 0.1% of benign tumors of the larynx.

Objectives To report the first case of massive neck plexiform neurofibroma with intralaryngeal (supraglottic) extension in a 5-year-old boy with neurofibromatosis type 1 and to describe its treatment.

Resumed Report This massive plexiform neurofibroma was surgically removed, relieving its significant respiratory obstructive symptoms without recurrence to date.

Conclusion Massive neck plexiform neurofibroma with supraglottic part was found in a child with neurofibromatosis type 1; it should be included in differential diagnosis of stridor and neck mass in children. It was diagnosed and removed in early in childhood without recurrence.