Int Arch Otorhinolaryngol 2015; 19(04): 359-363
DOI: 10.1055/s-0034-1395791
Case Report
Thieme Publicações Ltda Rio de Janeiro, Brazil

Cochlear Implantation in Isolated Large Vestibular Aqueduct Syndrome: Report of Three Cases and Literature Review

Rabindra Pradhananga
1  Department of ENT-Head and Neck Surgery, Tribhuvan University Teaching Hospital, Kathmandu, Nepal
2  Department of Implantation Otology, Madras ENT Research Foundation, Chennai, Tamil Nadu, India
,
Kiran Natarajan
3  Department of Otorhinolaryngology, Madras ENT Research Foundation, Chennai, Tamil Nadu, India
,
AmarNath Devarasetty
3  Department of Otorhinolaryngology, Madras ENT Research Foundation, Chennai, Tamil Nadu, India
,
Mohan Kameswaran
2  Department of Implantation Otology, Madras ENT Research Foundation, Chennai, Tamil Nadu, India
› Author Affiliations
Further Information

Publication History

24 August 2014

11 October 2014

Publication Date:
14 November 2014 (eFirst)

  

Abstract

Introduction Large vestibular aqueduct syndrome (LVAS) is characterized by the enlargement of the vestibular aqueduct associated with sensorineural hearing loss. It is the most common radiographically detectable inner ear anomaly in congenital hearing loss. LVAS may occur as an isolated anomaly or in association with other inner ear malformations.

Objective To report three cases of isolated LVAS with a focus on preoperative assessment, surgical issues, and short-term postoperative follow-up with preliminary auditory habilitation outcomes.

Resumed Report One girl and two boys with LVAS were assessed and cochlear implantation was performed for each. Various ways of intraoperative management of cerebrospinal fluid gusher and postoperative care and outcomes are reported.

Conclusion Cochlear implantation in the deaf children with LVAS is feasible and effective.