Alopecia areata totalis bei 19-jähriger Patientin mit Mayer-Rokitansky-Küster-Hauser-Syndrom (MRKHS)

Zusammenfassung

Wir berichten über eine 19-jährige Patientin mit Mayer-Rokitansky-Küster-Hauser-Syndrom (MRKHS), bei der sich binnen zwei Monaten eine Alopecia areata totalis entwickelte.

Das seltene Syndrom wird vorgestellt und mögliche Zusammenhänge mit der Haarerkrankung sowie Behandlungsmöglichkeiten einschließlich der Methylprednisolon-Puls-Therapie werden diskutiert.

Abstract

We report on a 19-year-old female patient with Mayer-Rokitansky-Küster-Hauser syndrome (MRKHS), who developed within two months an alopecia areata totalis. This rare syndrome is presented and a possible relationship to the hair disease and therapeutic options including methylprednisolone pulse therapy are discussed.

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