Int Arch Otorhinolaryngol 2014; 18 - a2138
DOI: 10.1055/s-0034-1388905

Mucocele and Nasal Polyposis in Patient with Cystic Fibrosis—Result Postoperative Case Report

Luis Alan Cardoso de Melo 1, Carla Graciliano Arguello Nunes 1, Caroline Fernandes Rimoli 1, José Vicente Tagliarini 1, Renata Misuzaki Iyomasa 1, Thaís Gomes Abrahão Elias 1
  • 1Universidade Estadual Paulista (Unesp)

Introduction: Cystic fibrosis is one of the most prevalent autosomal recessive diseases in the Caucasian population. It has high morbidity and mortality because of chronic endobronchial infections associated with obstructive pulmonary disease and progressive intestinal malabsorption secondary to pancreatic insufficiency. Approximately, 70 to 100% of patients develop chronic rhinosinusitis and nasal polyposis which is present in 40% of cases.

Objective: This study aims to report a case of mucocele and nasal polyposis in patients with cystic fibrosis and postoperative results.

Resumed Report: A 5-year-old patient presented with cystic fibrosis carrier followed since birth. The complaint was that the patient was snoring daily since 8 months, restless sleep, nasal obstruction mostly right, anterior rhinorrhea greenish left recursively.

Physical Examination: The patient had a high palate, teeth with diastema, presence of polypoid lesions obstructing the nostrils, hypertelorism, and asymmetry of the base of the nasal pyramid. Five months after the first follow-up, the patient was presented for resection of frontoethmoidal mucocele right and polypectomy bilateral. Significant improvement of preoperative complaints, keeping in nasal topical steroids.

Conclusion: Patients with cystic fibrosis initiate sinonasal complaints approximately at the age of 5 years, with formation of greenish secretions and thickened mainly in the maxillary sinus leading to formation of pseudomucoceles, medialization of the lateral wall, hypoplasia of the sphenoid and frontal sinuses, and nasal polyposis. Mucocele is rare in children and cystic fibrosis may be the only etiologic factor. In case of failures of clinical treatment indicated surgical procedure. Surgery varies from polypectomy to pansinusotomia, which is preferred by keeping the patient free most of the time for nasossinusal complaints.