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Semin Neurol 2014; 34(02): 121-128
DOI: 10.1055/s-0034-1381740
Thieme Medical Publishers 333 Seventh Avenue, New York, NY 10001, USA.

Historical Perspectives and Memories of Progressive Supranuclear Palsy

John C. Steele
1   Micronesian Health Study II, Guam
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Publikationsdatum:
25. Juni 2014 (online)

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Abstract

Parkinsonism recalls James Parkinson of London and his description of six patients with “paralysis agitans” in 1817, which neurologist Jean-Marie Charcot renamed Parkinson disease. Its variants, referred to as atypical parkinsonian disorders, are the subject of this issue of Seminars in Neurology through which we continue a journey toward understanding the pathogenesis of these diverse neurodegenerative diseases that are sometimes genetically determined, but are more often sporadic and without familial occurrence.

Keywords

progressive supranuclear palsy - tauopathy - amyotrophic lateral sclerosis/parkinsonism dementia complex - prion
 

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