Solitary Fibrous Tumor, Haemangioperycitoma and Sarcomatous Degeneration in the Same Patient. Case Report

The solitary fibrous tumor is an infrequent benign intracranial lesion, however there are descriptions of a locally agressive behavior with potential for sarcomatous degeneration and low evidence of complementary treatment options besides surgical resection.

We report the case of a 43 year old female, who presents a left frontal lesion, then undergoes a deformity on her face with proptosis and dyplopia months after the first resection is performed, associated with a new tumor. Afterwards, she presents a third tumor localized at the contralateral temporal fossa which is asymptomatic. The respective pathology reports were:haemangioperycitoma, solitary fibrous tumor and fusocellular sarcoma.

We performed 3 surgical resections with complete macroscopic removal of the tumors and drilling of the adjacent skull. A cosmetic reconstruction with cranioplasty and complementary treatment with radiotherapy and chemotherapy was administered after the first surgical resection.

The solitary fibrous tumor can show a locally aggressive and invasive behavior without a favorable response to complete surgical resection with a high risk for progression and a low progression-free interval despite first line treatment, which is the reason it is considered a pathology with poor outcome.