J Neurol Surg B 2014; 75 - A176
DOI: 10.1055/s-0034-1370582

Solitary Fibrous Tumor, Haemangioperycitoma and Sarcomatous Degeneration in the Same Patient. Case Report

Óscar Feo Lee 1, Juan Carlos Acevedo González 1, Roberto Díaz Orduz 1, Miguel Berbeo Calderón 1, Óscar Zorro Guío 1, Laura Díaz S. 1, Rafael Uribe C. 1, Jaime Becerra O. 1, Silvia Quintero O. 1, Juan Pérez R. 1, Pablo Harker F. 1
  • 1Bogotá, CO

The solitary fibrous tumor is an infrequent benign intracranial lesion, however there are descriptions of a locally agressive behavior with potential for sarcomatous degeneration and low evidence of complementary treatment options besides surgical resection.

We report the case of a 43 year old female, who presents a left frontal lesion, then undergoes a deformity on her face with proptosis and dyplopia months after the first resection is performed, associated with a new tumor. Afterwards, she presents a third tumor localized at the contralateral temporal fossa which is asymptomatic. The respective pathology reports were:haemangioperycitoma, solitary fibrous tumor and fusocellular sarcoma.

We performed 3 surgical resections with complete macroscopic removal of the tumors and drilling of the adjacent skull. A cosmetic reconstruction with cranioplasty and complementary treatment with radiotherapy and chemotherapy was administered after the first surgical resection.

The solitary fibrous tumor can show a locally aggressive and invasive behavior without a favorable response to complete surgical resection with a high risk for progression and a low progression-free interval despite first line treatment, which is the reason it is considered a pathology with poor outcome.