Right Bochdalek Hernia Associated with Kartagener Syndrome: Developmental and Clinical Observations

Abstract

We present a novel case of the association of right-sided Bochdalek hernia, a diaphragmatic life-threatening malformation, and Kartagener syndrome, which is characterized by congenital bronchiectasis, chronic sinusitis, and situs inversus. The developmental and clinical findings are discussed. When an association of diaphragmatic hernia with situs viscerum inversus is encountered, physicians should be mindful of the possibility of Kartagener syndrome because this condition could significantly affect the morbidity of the patient.

Keywords

Bochdalek hernia - Kartagener syndrome - diaphragm development

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