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Semin Plast Surg 2012; 26(02): 064-075
DOI: 10.1055/s-0032-1320064
Thieme Medical Publishers 333 Seventh Avenue, New York, NY 10001, USA.

Syndromic Craniosynostosis

Christopher Derderian
1   Department of Plastic Surgery, University of Texas Southwestern Medical Center, Dallas, Texas
,
James Seaward
1   Department of Plastic Surgery, University of Texas Southwestern Medical Center, Dallas, Texas
› Author Affiliations
Further Information

Publication History

Publication Date:
12 July 2012 (online)

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Abstract

Although most cases of craniosynostosis are nonsyndromic, craniosynostosis is known to occur in conjunction with other anomalies in well-defined patterns that make up clinically recognized syndromes. Patients with syndromic craniosynostoses are much more complicated to care for, requiring a multidisciplinary approach to address all of their needs effectively.

This review describes the most common craniosynostosis syndromes, their characteristic features and syndrome-specific functional issues, and new modalities utilized in their management. General principles including skull development, the risk of developing increased intracranial pressure in craniosynostosis syndromes, and techniques to measure intracranial pressure are discussed. Evolving techniques of the established operative management of craniosynostosis are discussed together with more recent techniques including spring cranioplasty and posterior cranial vault distraction osteogenesis.

Keywords

syndromic craniosynostosis - intracranial pressure - posterior vault distraction - spring cranioplasty - midface distraction
 

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