Malignant Progression of Anaplastic Supratentorial Ganglioglioma into Glioblastoma Multiforme in a Patient with Turner Syndrome^[*]

Introduction

Gangliogliomas (GGs) of the central nervous system (CNS) are rather uncommon lesions comprising approximately 1% of all brain neoplasms. The malignant variants of these tumors are extremely rare.[1] [2] Here, we describe a unique case of a 36-year-old female with known Turner syndrome (TS) in association with primary anaplastic supratentorial GG.

^* This article was originally published online in Central European Neurosurgery on December 17, 2010 (DOI:10.1055/s-0030-1268497)

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