Abstract
Pheochromocytoma and paraganglioma are rare tumors of sympathetic or parasympathetic
origin, presenting with a highly variable clinical picture. Rarity, as well as biological,
clinical, and genetic heterogeneity are barriers to initiate prospective studies that
help to establish clinical guidelines. The best management of these patients relies
on the experience of a multidisciplinary team. The ultimate outcome can benefit from
adequate pre-surgical evaluation and treatment as well as an accurate post-surgical
follow-up. Long-term follow-up is mandatory in all patients, but is particularly important
in specific familial cases such as those with an SDHB mutation where the risks of
recurrence are higher. The surgical approach varies depending on tumor size, location,
and surgeon’s personal attitude and experience. In this paper, we summarize recommendations,
based mostly on authors’ and other experts’ personal experiences, for the best possible
management of patients prior, during and after surgery, as well as when pheochromocytoma
is diagnosed during pregnancy.
Key words
pheochromocytoma - anesthesia - surgery - pregnancy
