Abstract
Deep vein thrombosis is a frequent finding in otherwise healthy, young adults who are diagnosed with congenital absence (agenesis) of the inferior vena cava - a rare anomaly. This condition is best diagnosed by computed tomography angiography with venous phase imaging, and is managed using anticoagulation, percutaneous catheter-directed mechanical thrombectomy and thrombolysis. To illustrate this phenomenon, a case is presented.